We report on a rare case of a child with persistent right upper lid eversion with conjunctival prolapse since birth that
failed various attempts in repositioning the right superior fornix at other centre. He was found to have a right superotemporal
orbital mass above the prolapsed area. Computerized tomography (CT) scan of orbit confirmed a right
lacrimal gland tumour with thinning of the right lesser wing of sphenoid. An excision biopsy of the tumour via
anterior orbitotomy and eyelid reconstruction were performed. Histopathology report reviewed plexiform
neurofibroma of the lacrimal gland. Further physical examination confirmed presence of multiple café-au-lait spots.
He was diagnosed as Neurofibromatosis Type 1.