Affiliations 

  • 1 Endocrinology Unit, Department of Medicine, Hospital Tuanku Ja'afar Seremban, Malaysia
  • 2 Haematology Unit, Department of Medicine, Hospital Tuanku Ja'afar Seremban, Malaysia
J ASEAN Fed Endocr Soc, 2021;36(1):80-84.
PMID: 34177092 DOI: 10.15605/jafes.036.01.04

Abstract

Extramedullary hematopoiesis (EMH) is a rare cause of adrenal mass. We present a 44-year-old woman who has thalassaemia intermedia, referred to Endocrinology clinic for huge adrenal mass. Along with a paraspinal lesion discovered in this patient, the leading diagnosis was EMH. The patient was treated with hypertransfusion and hydroxyurea, which led to a reduction in the size of the right adrenal mass and paraspinal mass. This case highlights the challenges in managing this rare condition. Although EMH is a rare cause of adrenal mass, the diagnosis must be considered in any patient with a history of a congenital hemolytic disorder, to avoid unnecessary surgical procedures.

* Title and MeSH Headings from MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine.