Affiliations 

  • 1 Department of O&G, Ministry of Health, Hospital Sultanah Nur Zahirah/Hospital Kemaman, Kuala Terengganu/Kemaman, Malaysia
  • 2 Department of O&G, Ministry of Health, Hospital Sultanah Nur Zahirah/Hospital Kemaman, Kuala Terengganu/Kemaman, Malaysia drroziana@yahoo.com
BMJ Case Rep, 2024 May 22;17(5).
PMID: 38782440 DOI: 10.1136/bcr-2024-259861

Abstract

Obstructed Hemi Vagina with Ipsilateral Renal Agenesis (OHVIRA) syndrome is a rarely encountered müllerian duct anomaly. Delayed diagnosis is common due to normal onset of puberty and menstruation. We report a case of a woman in her early 20s with a background history of multiple emergency department visits, ward admissions and surgeries for chronic abdominal pain. She was reviewed at 1 month postlaparotomy for recurrent pelvic abscess and was finally diagnosed to have an OHVIRA syndrome, 11 years after her first clinical presentation. Excision of the vaginal septum completely resolved her symptoms. We are reporting this case to highlight the clinical implications resulting from the delayed diagnosis, to look into factors contributing to the delay and to highlight the importance of having a high index of suspicion to diagnose this unique condition.

* Title and MeSH Headings from MEDLINE®/PubMed®, a database of the U.S. National Library of Medicine.